The Scottish Renal Registry



ERA-EDTA Primary Renal Diagnosis Codes, and Groupings used in SRR analyses


PDF ERA-EDTA Primary Renal Diagnosis Codes and Groupings

PDF Cause of Dealth Codes and Groups

Primary Renal Diagnosis Codes & Groupings

Group 1: Primary Glomerulonephritis
3749 
Glomerulonephritis - no histology
1003 
Adult nephrotic syndrome - no histology
1019
Nephrotic syndrome of childhood - steriod sensitive - no histology
3604
Nephrotic syndrome of childhood - steriod resistant - no histology
3615
Nephrotic syndrome of childhood - no trial of steriods - no histology
1026
Congenital nephrotic syndrome (CNS) - no histology
1035
Congenital nephrotic syndrome (CNS) - Finnish Type - no histology
1042
Congenital nephrotic syndrome (CNS) - Finnish Type - histologically proven
1057
Congenital nephrotic syndrome (CNS) - diffuse mesangial sclerosis
1061
Congenital nephrotic syndrome (CNS) - focal segmental glomerulosclerosis (FSGS)
1074
Denys-Drash syndrome
1088
Congenital nephrotic syndrome (CNS) - congenital infection
1090
Minimal change nephropathy - no histology
1100
Minimal change nephropathy - histologically proven
1116
IgA nephropathy - no histology
1128
IgA nephropathy - histologically proven
1137
Familial IgA nephropathy - no histology
1144
Familial IgA nephropathy - histologically proven
1159
IgA nephropathy secondary to liver cirrhosis - no histology
1163
IgA nephropathy secondary to liver cirrhosis - histologically proven
1171
IgM - associated nephropathy
1185
Membranous nephropathy - idiopathic
1192
Membranous nephropathy - malignancy associated
1205
Membranous nephropathy - drug induced
1214
Membranous nephropathy - infection associated
1222
Mesangiocapillary glomerulonenephritis type 1
1233
Mesangiocapillary glomerulonenephritis type 2 (dense deposit disease)
1246
Mesangiocapillary glomerulonenephritis type 3
1251
Idiopathic rapidly progressive (crescentic) glomerulonephritis
1267
Primary focal segmental glomerulosclerosis (FSGS)
1279
Familial focal segmental glomerulosclerosis (FSGS) autosomal recessive - no histology
1280
Familial focal segmental glomerulosclerosis (FSGS) autosomal recessive - histologically proven
1298
Familial focal segmental glomerulosclerosis (FSGS) - autosomal dominant - no histology
1308
Familial focal segmental glomerulosclerosis (FSGS) - autosomal dominant - histologically proven
1312
Focal segmental glomerulosclerosis (FSGS) - secondary to obesity - no histology
1320
Focal segmental glomerulosclerosis (FSGS) - secondary to obesity - histologically proven
3754
Focal segmental glomerulosclerosis (FSGS) - secondary to HIV
3765
Focal segmental glomerulosclerosis (FSGS) - secondary to lithium
3777
Focal segmental glomerulosclerosis (FSGS) - secondary to sickle cell
1331
Diffuse endocapillary glomerulonephritis
1349
Mesangial proliferative glomerulonephritis
1354
Focal and segmental proliferative glomerulonephritis
1365
Glomerulonephritis - secondary to other systemic disease
1377
Glomerulonephritis - histologically indeterminate
2606
Immunotactoid / fibrillary nephropathy

Group 2: Interstitial Nephropathies
1602
Primary reflux nephropathy - sporadic
1618
Familial reflux nephropathy
1625
Congenital dysplasia / hypoplasia
1639
Multicystic dysplastic kidneys
1641
Dysplasia due to fetal ACE-inhibitor exposure
1656
Glomerulocystic disease
1660
Congenital pelvi-ureteric junction obstruction
1673
Congenital vesico-ureteric junction obstruction
1687
Posterior urethral valves
1694
Syndrome of agenesis of abdominal muscles - prune belly syndrome
1706
Congenital neurogenic bladder
1710
Bladder exstrophy
1723
Megacystis-megaureter
1734
Oligomeganephronia
1747
Renal papillary necrosis - cause unknown
3783
Renal papillary necrosis - caused by diabetes
3796
Renal papillary necrosis - caused by analgesics
3806
Renal papillary necrosis - caused by sickle cell
3810
Kidney stones due to ARPT deficiency
1752
Acquired obstructive uropathy / nephropathy
1768
Acquired obstructive nephropathy due to neurogenic bladder
1775
Obstructive nephropathy due to prostatic hypertrophy
1781
Obstructive nephropathy due to prostrate cancer
1799
Obstructive nephropathy due to bladder cancer
1809
Obstructive nephropathy due to other malignancies
1813
Idiopathic retroperitoneal fibrosis
1821
Retroperitoneal fibrosis secondary to malignancies
3689
Retroperitoneal fibrosis secondary to drugs
3670
Retroperitoneal fibrosis secondary to peri-aortitis
1832
Calculus nephropathy / urolithiasis
1845
Calcium oxalate urolithiasis
1850
Enteric hyperoxaluria
1866
Magnesium ammonium phosphate (struvite) urolithiasis
1878
Uric acid urolithiasis
1884
Tubulointerstitial nephritis - no histology
1897
Tubulointerstitial nephritis - histologically proven
1907
Familial interstitial nephropathy - no histology
1911
Familial interstitial nephropathy - histologically proven
1924
Tubulointerstitial nephritis associated with autoimmune disease - no histology
1930
Tubulointerstitial nephritis associated with autoimmune disease - histologically proven
1948
Tubulointerstitial nephritis with uveitis (TINU) - no histology
1953
Tubulointerstitial nephritis with uveitis (TINU) - histologically proven
1969
Renal sarcoidosis - no histology
1976
Renal sarcoidosis - histologically proven
1982
Aristolochic acid nephropathy (Balkan / Chinese herb / endemic nephropathy) - no histology
1995
Aristolochic acid nephropathy (Balkan / Chinese herb / endemic nephropathy) - histologically proven
2005
Drug-induced tubulointerstitial nephritis  - no histology
2014
Drug-induced tubulointerstitial nephritis  - histologically proven
2022
Nephropathy due to analgesic drugs - no histology
2033
Nephropathy due to analgesic drugs - histologically proven
2046
Nephropathy due to ciclosporin - no histology
2051
Nephropathy due to ciclosporin - histologically proven
2067
Nephropathy due to tacrolimus - no histology
2079
Nephropathy due to tacrolimus - histologically proven
2080
Nephropathy due to aminoglycosides - no histology
2098
Nephropathy due to aminoglycosides - histologically proven
2108
Nephropathy due to amphotericin - no histology
2112
Nephropathy due to amphotericin - histologically proven
2120
Nephropathy due to cisplatin - no histology
2131
Nephropathy due to cisplatin - histologically proven
2149
Nephropathy due to lithium - no histology
2154
Nephropathy due to lithium - histologically proven
2165
Lead induced nephropathy - no histology
2177
Lead induced nephropathy - histologically proven
2183
Acute urate nephropathy - no histology
2196
Acute urate nephropathy - histologically proven
3636
Chronic urate nephropathy - no histology
2203
Chronic urate nephropathy - histologically proven
3662
Hypercalcaemic nephropathy
2219
Radiation nephritis
2226
Renal / perinephric abscess
2261
Xanthogranulomatous pyelonephritis
2718
Autosomal dominant (AD) polycystic kidney disease
2725
Autosomal dominant (AD) polycystic kidney disease type I
2739
Autosomal dominant (AD) polycystic kidney disease type II
2741
Autosomal recessive (AR) polycystic kidney disease
2756
Alport syndrome - no histology
2760
Alport syndrome - histologically proven
2794
Cystic kidney disease
2804
Medullary cystic kidney disease type I
2815
Medullary cystic kidney disease type II
2827
Uromodulin-associated nephropathy (familial juvenile hyperuricaemic nephropathy)
2836
Nephronophthisis
2843
Nephronophthisis - type 1 (juvenile type)
2858
Nephronophthisis - type 2 (infantile type)
2862
Nephronophthisis - type 3 (adolescent type)
2870
Nephronophthisis - type 4 (juvenile type)
2889
Nephronophthisis - type 5
2891
Nephronophthisis - type 6
2901
Primary Fanconi syndrome
2917
Tubular disorder as part of inherited metabolic diseases
2929
Dent disease
2938
Lowe syndrome (oculocerebrorenal syndrome)
2940
Inherited aminoaciduria
2955
Cystinuria
2964
Cystinosis
2972
Inherited renal glycosuria
2986
Hypophosphataemic rickets X-linked (XL)
2993
Hypophosphataemic rickets autosomal recessive (AR)
3000
Primary renal tubular acidosis (RTA)
3016
Proximal renal tubular acidosis (RTA) - type II
3028
Distal renal tubular acidosis (RTA) - type I
3037
Distal renal tubular acidosis with sensorineural deafness - gene mutations
3044
Nephrogenic diabetes insipidus
3059
Lesch Nyhan syndrome - hypoxanthine guanine phosphoribosyl transferase deficiency
3063
Phosphoribosyl pyrophosphate synthetase (PRPPS) superactivity
3071
Alagille syndrome
3085
Bartter syndrome
3092
Gitelman syndrome
3102
Liddle syndrome
3118
Apparent mineralocorticoid excess
3125
Glucocorticoid suppressible hyperaldosteronism
3141
Pseudohypoaldosteronism type 1
3156
Pseudohypoaldosteronism type 1 (Gordon syndrome)
3160
Familial hypocalciuric hypercalcaemia
3173
Familial hypercalciuric hypocalcaemia
3187
Familial hypomagnesaemia
3194
Primary hyperoxaluria
3207
Primary hyperoxaluria type I
3211
Primary hyperoxaluria type II
3731
Primary hyperoxaluria type III
3224
Fabry disease - no histology
3230
Fabry disease - histologically proven
3248
Xanthinuria
3253
Nail-patella syndrome
3269
Rubinstein-Taybi syndrome
3276
Tuberous sclerosis
3282
Von Hippel-Lindau disease
3295
Medullary sponge kidneys
3305
Horse-shoe kidney
3314
Frasier syndrome
3658
Renal coloboma syndrome
3322
Branchio-oto-renal syndrome
3333
Williams syndrome
3346
Townes-Brocks syndrome
3351
Lawrence-Moon-Biedl / Bardet-Biedl syndrome
3367
Mitochondrial cytopathy
3379
Familial nephropathy
3457
Acute pyelonephritis

Group 3: Multisystem Diseases
1383
Systemic vasculitis - ANCA negative - histologically proven
1396
Systemic vasculitis - ANCA positive - no histology
1401
Granulomatosis with polyangiitis - no histology
1417
Granulomatosis with polyangiitis - histologically proven
1429
Microscopic polyangiitis - histologically proven
1438
Churg-Strauss syndrome - no histology
1440
Churg-Strauss syndrome - histologically proven
1455
Polyarteritis nodosa
1464
Anti-Glomerular basement membrane (GBM) disease / Goodpasture's syndrome - no histology
1472
Anti-Glomerular basement membrane (GBM) disease / Goodpasture's syndrome - histologically proven
1486
Systemic lupus erythematosus / nephritis - no histology
1493
Systemic lupus erythematosus / nephritis - histologically proven
1504
Henoch-Schönlein purpura / nephritis - no histology
1515
Henoch-Schönlein purpura / nephritis - histologically proven
1527
Renal scleroderma / systemic sclerosis - no histology
1536
Renal scleroderma / systemic sclerosis - histologically proven
1543
Essential mixed cryoglobulinaemia - no histology
1558
Essential mixed cryoglobulinaemia - histologically proven
1562
Cryoglobulinaemia secondary to hepatitis C - no histology
1570
Cryoglobulinaemia secondary to hepatitis C - histologically proven
1589
Cryoglobulinaemia secondary to systemic disease - no histology
1591
Cryoglobulinaemia secondary to systemic disease - histologically proven
2235
Renal tuberculosis
2242
Leptospirosis
2257
Hantavirus nephropathy
2274
Nephropathy related to HIV - no histology
2288
Nephropathy related to HIV - histologically proven
3834
Nephropathy due to pre-eclampsia
2290
Schistosomiasis
2300
Other specific infection
2359
Chronic hypertensive nephropathy - no histology
2363
Chronic hypertensive nephropathy - histologically proven
2371
Malignant hypertensive nephropathy / accelerated hypertensive nephropathy - no histology
2385
Malignant hypertensive nephropathy / accelerated hypertensive nephropathy - histologically proven
2392
Ageing kidney - no histology
2407
Ischaemic nephropathy - no histology
2411
Ischaemic nephropathy / microvascular disease - histologically proven
2424
Renal artery stenosis
2430
Atheroembolic renal disease - no histology
2448
Atheroembolic renal disease - histologically proven
2453
Fibromuscular dysplasia of renal artery
2469
Renal arterial thrombosis / occlusion
2482
Cardiorenal syndrome
2495
Hepatorenal syndrome
2509
Renal amyloidosis
2513
AA amyloid secondary to chronic inflammation
2521
AL amyloid secondary to plasma cell dyscrasia
2532
Familial amyloid secondary to protein mutations - no histology
2545 Familial amyloid secondary to protein mutations - histologically proven
2550
Familial AA amyloid secondary to familial Mediterranean fever / TRAPS (Hibernian fever) - no histology
2566
Familial AA amyloid secondary to familial Mediterranean fever / TRAPS (Hibernian fever) - histologically proven
2578
Myeloma kidney - no histology
2584
Myeloma cast nephropathy - histologically proven
2597
Light chain deposition disease
2610
Haemolytic uraemic syndrome (HUS) - diarrhoea associated
2623
Atypical haemolytic uraemic syndrome (HUS) - diarrhoea negative
2634
Thrombotic thrombocytopenic purpura (TTP)
2647
Haemolytic uraemic syndrome (HUS) secondary to systemic disease
2652
Congenital haemolytic uraemic syndrome (HUS)
2668
Familial haemolytic uraemic syndrome (HUS)
2675
Familial thrombotic thrombocytopenic purpura (TTP)
2681
Nephropathy due to eclampsia
2699
Sickle cell nephropathy - no histology
2702
Sickle cell nephropathy - histologically proven
3380
Acute kidney injury
3398
Acute kidney injury due to hypovolaemia 
3403
Acute kidney injury due to circulatory failure
3419
Acute kidney injury due to sepsis
3426
Acute kidney injury due to rhabdomyolysis
3435
Acute kidney injury due to nephrotoxicity
3442
Acute cortical necrosis
3461
Kidney tumour
3474
Renal cell carcinoma - histologically proven
3488
Transitional cell carcinoma - histologically proven
3490
Wilms tumour - histologically proven
3501
Mesoblastic nephroma - histologically proven
3529
Chronic kidney disease (CKD) / chronic renal failure (CRF) caused by tumour nephrectomy
3538
Chronic kidney disease (CKD) / chronic renal failure (CRF) due to traumatic loss of kidney
3643
Chronic renal failure due to systemic infection

Group 4: - Diabetic Nephropathy
2316
Diabetic nephropathy in type I diabetes - no histology
2328
Diabetic nephropathy in type I diabetes - histologically proven
2337
Diabetic nephropathy in type II diabetes - no histology
2344
Diabetic nephropathy in type II diabetes - histologically proven
3139
Inherited / genetic diabetes mellitus type II

Group 5: - Not Known and Other
3627
Renal cysts and diabetes syndrome
2476
Renal vein thrombosis
2773
Benign familial haematuria
2787
Thin basement membrane disease
3517
Single kidney identified in adulthood
3540
Chronic kidney disease (CKD) / chronic renal failure (CRF) due to donor nephrectomy
3555
Chronic kidney disease (CKD) / chronic renal failure (CRF) - aetiology uncertain / unknown - no histology
3564
Chronic kidney disease (CKD) / chronic renal failure (CRF) - aetiology uncertain / unknown - histologically proven
3572
Haematuria and proteinuria - no histology
3712
Isolated haematuria - no histology
3720
Isolated proteinuria - no histology
3691
Renal failure
3708
Chronic renal failure