Last updated: November 10, 2020
Group
1: Primary Glomerulonephritis |
Group
2: Interstitial Nephropathies |
Group
3: Multisystem Diseases |
Group
4: Diabetic Nephropathy |
Group
5: Not Known and Other |
ERA-EDTA Primary Renal Diagnosis Codes and Groupings
Cause of Dealth Codes and Groups
Group 1: Primary Glomerulonephritis |
|
3749 |
Glomerulonephritis - no histology |
1003 |
Adult nephrotic syndrome - no histology |
1019 |
Nephrotic syndrome of childhood - steriod sensitive - no histology |
3604 |
Nephrotic syndrome of childhood - steriod resistant - no histology |
3615 |
Nephrotic syndrome of childhood - no trial of steriods - no histology |
1026 |
Congenital nephrotic syndrome (CNS) - no histology |
1035 |
Congenital nephrotic syndrome (CNS) - Finnish Type - no histology |
1042 |
Congenital nephrotic syndrome (CNS) - Finnish Type - histologically proven |
1057 |
Congenital nephrotic syndrome (CNS) - diffuse mesangial sclerosis |
1061 |
Congenital nephrotic syndrome (CNS) - focal segmental glomerulosclerosis (FSGS) |
1074 |
Denys-Drash syndrome |
1088 |
Congenital nephrotic syndrome (CNS) - congenital infection |
1090 |
Minimal change nephropathy - no histology |
1100 |
Minimal change nephropathy - histologically proven |
1116 |
IgA nephropathy - no histology |
1128 |
IgA nephropathy - histologically proven |
1137 |
Familial IgA nephropathy - no histology |
1144 |
Familial IgA nephropathy - histologically proven |
1159 |
IgA nephropathy secondary to liver cirrhosis - no histology |
1163 |
IgA nephropathy secondary to liver cirrhosis - histologically proven |
1171 |
IgM - associated nephropathy |
1185 |
Membranous nephropathy - idiopathic |
1192 |
Membranous nephropathy - malignancy associated |
1205 |
Membranous nephropathy - drug induced |
1214 |
Membranous nephropathy - infection associated |
1222 |
Mesangiocapillary glomerulonenephritis type 1 |
1233 |
Mesangiocapillary glomerulonenephritis type 2 (dense deposit disease) |
1246 |
Mesangiocapillary glomerulonenephritis type 3 |
1251 |
Idiopathic rapidly progressive (crescentic) glomerulonephritis |
1267 |
Primary focal segmental glomerulosclerosis (FSGS) |
1279 |
Familial focal segmental glomerulosclerosis (FSGS) autosomal recessive - no histology |
1280 |
Familial focal segmental glomerulosclerosis (FSGS) autosomal recessive - histologically proven |
1298 |
Familial focal segmental glomerulosclerosis (FSGS) - autosomal dominant - no histology |
1308 |
Familial focal segmental glomerulosclerosis (FSGS) - autosomal dominant - histologically proven |
1312 |
Focal segmental glomerulosclerosis (FSGS) - secondary to obesity - no histology |
1320 |
Focal segmental glomerulosclerosis (FSGS) - secondary to obesity - histologically proven |
3754 |
Focal segmental glomerulosclerosis (FSGS) - secondary to HIV |
3765 |
Focal segmental glomerulosclerosis (FSGS) - secondary to lithium |
3777 |
Focal segmental glomerulosclerosis (FSGS) - secondary to sickle cell |
1331 |
Diffuse endocapillary glomerulonephritis |
1349 |
Mesangial proliferative glomerulonephritis |
1354 |
Focal and segmental proliferative glomerulonephritis |
1365 |
Glomerulonephritis - secondary to other systemic disease |
1377 |
Glomerulonephritis - histologically indeterminate |
2606 |
Immunotactoid / fibrillary nephropathy |
1602 |
Primary reflux nephropathy - sporadic |
1618 |
Familial reflux nephropathy |
1625 |
Congenital dysplasia / hypoplasia |
1639 |
Multicystic dysplastic kidneys |
1641 |
Dysplasia due to fetal ACE-inhibitor exposure |
1656 |
Glomerulocystic disease |
1660 |
Congenital pelvi-ureteric junction obstruction |
1673 |
Congenital vesico-ureteric junction obstruction |
1687 |
Posterior urethral valves |
1694 |
Syndrome of agenesis of abdominal muscles - prune belly syndrome |
1706 |
Congenital neurogenic bladder |
1710 |
Bladder exstrophy |
1723 |
Megacystis-megaureter |
1734 |
Oligomeganephronia |
1747 |
Renal papillary necrosis - cause unknown |
3783 |
Renal papillary necrosis - caused by diabetes |
3796 |
Renal papillary necrosis - caused by analgesics |
3806 |
Renal papillary necrosis - caused by sickle cell |
3810 |
Kidney stones due to ARPT deficiency |
1752 |
Acquired obstructive uropathy / nephropathy |
1768 |
Acquired obstructive nephropathy due to neurogenic bladder |
1775 |
Obstructive nephropathy due to prostatic hypertrophy |
1781 |
Obstructive nephropathy due to prostrate cancer |
1799 |
Obstructive nephropathy due to bladder cancer |
1809 |
Obstructive nephropathy due to other malignancies |
1813 |
Idiopathic retroperitoneal fibrosis |
1821 |
Retroperitoneal fibrosis secondary to malignancies |
3689 |
Retroperitoneal fibrosis secondary to drugs |
3670 |
Retroperitoneal fibrosis secondary to peri-aortitis |
1832 |
Calculus nephropathy / urolithiasis |
1845 |
Calcium oxalate urolithiasis |
1850 |
Enteric hyperoxaluria |
1866 |
Magnesium ammonium phosphate (struvite) urolithiasis |
1878 |
Uric acid urolithiasis |
1884 |
Tubulointerstitial nephritis - no histology |
1897 |
Tubulointerstitial nephritis - histologically proven |
1907 |
Familial interstitial nephropathy - no histology |
1911 |
Familial interstitial nephropathy - histologically proven |
1924 |
Tubulointerstitial nephritis associated with autoimmune disease - no histology |
1930 |
Tubulointerstitial nephritis associated with autoimmune disease - histologically proven |
1948 |
Tubulointerstitial nephritis with uveitis (TINU) - no histology |
1953 |
Tubulointerstitial nephritis with uveitis (TINU) - histologically proven |
1969 |
Renal sarcoidosis - no histology |
1976 |
Renal sarcoidosis - histologically proven |
1982 |
Aristolochic acid nephropathy (Balkan / Chinese herb / endemic nephropathy) - no histology |
1995 |
Aristolochic acid nephropathy (Balkan / Chinese herb / endemic nephropathy) - histologically proven |
2005 |
Drug-induced tubulointerstitial nephritis - no histology |
2014 |
Drug-induced tubulointerstitial nephritis - histologically proven |
2022 |
Nephropathy due to analgesic drugs - no histology |
2033 |
Nephropathy due to analgesic drugs - histologically proven |
2046 |
Nephropathy due to ciclosporin - no histology |
2051 |
Nephropathy due to ciclosporin - histologically proven |
2067 |
Nephropathy due to tacrolimus - no histology |
2079 |
Nephropathy due to tacrolimus - histologically proven |
2080 |
Nephropathy due to aminoglycosides - no histology |
2098 |
Nephropathy due to aminoglycosides - histologically proven |
2108 |
Nephropathy due to amphotericin - no histology |
2112 |
Nephropathy due to amphotericin - histologically proven |
2120 |
Nephropathy due to cisplatin - no histology |
2131 |
Nephropathy due to cisplatin - histologically proven |
2149 |
Nephropathy due to lithium - no histology |
2154 |
Nephropathy due to lithium - histologically proven |
2165 |
Lead induced nephropathy - no histology |
2177 |
Lead induced nephropathy - histologically proven |
2183 |
Acute urate nephropathy - no histology |
2196 |
Acute urate nephropathy - histologically proven |
3636 |
Chronic urate nephropathy - no histology |
2203 |
Chronic urate nephropathy - histologically proven |
3662 |
Hypercalcaemic nephropathy |
2219 |
Radiation nephritis |
2226 |
Renal / perinephric abscess |
2261 |
Xanthogranulomatous pyelonephritis |
2718 |
Autosomal dominant (AD) polycystic kidney disease |
2725 |
Autosomal dominant (AD) polycystic kidney disease type I |
2739 |
Autosomal dominant (AD) polycystic kidney disease type II |
2741 |
Autosomal recessive (AR) polycystic kidney disease |
2756 |
Alport syndrome - no histology |
2760 |
Alport syndrome - histologically proven |
2794 |
Cystic kidney disease |
2804 |
Medullary cystic kidney disease type I |
2815 |
Medullary cystic kidney disease type II |
2827 |
Uromodulin-associated nephropathy (familial juvenile hyperuricaemic nephropathy) |
2836 |
Nephronophthisis |
2843 |
Nephronophthisis - type 1 (juvenile type) |
2858 |
Nephronophthisis - type 2 (infantile type) |
2862 |
Nephronophthisis - type 3 (adolescent type) |
2870 |
Nephronophthisis - type 4 (juvenile type) |
2889 |
Nephronophthisis - type 5 |
2891 |
Nephronophthisis - type 6 |
2901 |
Primary Fanconi syndrome |
2917 |
Tubular disorder as part of inherited metabolic diseases |
2929 |
Dent disease |
2938 |
Lowe syndrome (oculocerebrorenal syndrome) |
2940 |
Inherited aminoaciduria |
2955 |
Cystinuria |
2964 |
Cystinosis |
2972 |
Inherited renal glycosuria |
2986 |
Hypophosphataemic rickets X-linked (XL) |
2993 |
Hypophosphataemic rickets autosomal recessive (AR) |
3000 |
Primary renal tubular acidosis (RTA) |
3016 |
Proximal renal tubular acidosis (RTA) - type II |
3028 |
Distal renal tubular acidosis (RTA) - type I |
3037 |
Distal renal tubular acidosis with sensorineural deafness - gene mutations |
3044 |
Nephrogenic diabetes insipidus |
3059 |
Lesch Nyhan syndrome - hypoxanthine guanine phosphoribosyl transferase deficiency |
3063 |
Phosphoribosyl pyrophosphate synthetase (PRPPS) superactivity |
3071 |
Alagille syndrome |
3085 |
Bartter syndrome |
3092 |
Gitelman syndrome |
3102 |
Liddle syndrome |
3118 |
Apparent mineralocorticoid excess |
3125 |
Glucocorticoid suppressible hyperaldosteronism |
3141 |
Pseudohypoaldosteronism type 1 |
3156 |
Pseudohypoaldosteronism type 1 (Gordon syndrome) |
3160 |
Familial hypocalciuric hypercalcaemia |
3173 |
Familial hypercalciuric hypocalcaemia |
3187 |
Familial hypomagnesaemia |
3194 |
Primary hyperoxaluria |
3207 |
Primary hyperoxaluria type I |
3211 |
Primary hyperoxaluria type II |
3731 |
Primary hyperoxaluria type III |
3224 |
Fabry disease - no histology |
3230 |
Fabry disease - histologically proven |
3248 |
Xanthinuria |
3253 |
Nail-patella syndrome |
3269 |
Rubinstein-Taybi syndrome |
3276 |
Tuberous sclerosis |
3282 |
Von Hippel-Lindau disease |
3295 |
Medullary sponge kidneys |
3305 |
Horse-shoe kidney |
3314 |
Frasier syndrome |
3658 |
Renal coloboma syndrome |
3322 |
Branchio-oto-renal syndrome |
3333 |
Williams syndrome |
3346 |
Townes-Brocks syndrome |
3351 |
Lawrence-Moon-Biedl / Bardet-Biedl syndrome |
3367 |
Mitochondrial cytopathy |
3379 |
Familial nephropathy |
3457 |
Acute pyelonephritis |
1383 |
Systemic vasculitis - ANCA negative - histologically proven |
1396 |
Systemic vasculitis - ANCA positive - no histology |
1401 |
Granulomatosis with polyangiitis - no histology |
1417 |
Granulomatosis with polyangiitis - histologically proven |
1429 |
Microscopic polyangiitis - histologically proven |
1438 |
Churg-Strauss syndrome - no histology |
1440 |
Churg-Strauss syndrome - histologically proven |
1455 |
Polyarteritis nodosa |
1464 |
Anti-Glomerular basement membrane (GBM) disease / Goodpasture's syndrome - no histology |
1472 |
Anti-Glomerular basement membrane (GBM) disease / Goodpasture's syndrome - histologically proven |
1486 |
Systemic lupus erythematosus / nephritis - no histology |
1493 |
Systemic lupus erythematosus / nephritis - histologically proven |
1504 |
Henoch-Schönlein purpura / nephritis - no histology |
1515 |
Henoch-Schönlein purpura / nephritis - histologically proven |
1527 |
Renal scleroderma / systemic sclerosis - no histology |
1536 |
Renal scleroderma / systemic sclerosis - histologically proven |
1543 |
Essential mixed cryoglobulinaemia - no histology |
1558 |
Essential mixed cryoglobulinaemia - histologically proven |
1562 |
Cryoglobulinaemia secondary to hepatitis C - no histology |
1570 |
Cryoglobulinaemia secondary to hepatitis C - histologically proven |
1589 |
Cryoglobulinaemia secondary to systemic disease - no histology |
1591 |
Cryoglobulinaemia secondary to systemic disease - histologically proven |
2235 |
Renal tuberculosis |
2242 |
Leptospirosis |
2257 |
Hantavirus nephropathy |
2274 |
Nephropathy related to HIV - no histology |
2288 |
Nephropathy related to HIV - histologically proven |
3834 |
Nephropathy due to pre-eclampsia |
2290 |
Schistosomiasis |
2300 |
Other specific infection |
2359 |
Chronic hypertensive nephropathy - no histology |
2363 |
Chronic hypertensive nephropathy - histologically proven |
2371 |
Malignant hypertensive nephropathy / accelerated hypertensive nephropathy - no histology |
2385 |
Malignant hypertensive nephropathy / accelerated hypertensive nephropathy - histologically proven |
2392 |
Ageing kidney - no histology |
2407 |
Ischaemic nephropathy - no histology |
2411 |
Ischaemic nephropathy / microvascular disease - histologically proven |
2424 |
Renal artery stenosis |
2430 |
Atheroembolic renal disease - no histology |
2448 |
Atheroembolic renal disease - histologically proven |
2453 |
Fibromuscular dysplasia of renal artery |
2469 |
Renal arterial thrombosis / occlusion |
2482 |
Cardiorenal syndrome |
2495 |
Hepatorenal syndrome |
2509 |
Renal amyloidosis |
2513 |
AA amyloid secondary to chronic inflammation |
2521 |
AL amyloid secondary to plasma cell dyscrasia |
2532 |
Familial amyloid secondary to protein mutations - no histology |
2545 | Familial amyloid secondary to protein mutations - histologically proven |
2550 |
Familial AA amyloid secondary to familial Mediterranean fever / TRAPS (Hibernian fever) - no histology |
2566 |
Familial AA amyloid secondary to familial Mediterranean fever / TRAPS (Hibernian fever) - histologically proven |
2578 |
Myeloma kidney - no histology |
2584 |
Myeloma cast nephropathy - histologically proven |
2597 |
Light chain deposition disease |
2610 |
Haemolytic uraemic syndrome (HUS) - diarrhoea associated |
2623 |
Atypical haemolytic uraemic syndrome (HUS) - diarrhoea negative |
2634 |
Thrombotic thrombocytopenic purpura (TTP) |
2647 |
Haemolytic uraemic syndrome (HUS) secondary to systemic disease |
2652 |
Congenital haemolytic uraemic syndrome (HUS) |
2668 |
Familial haemolytic uraemic syndrome (HUS) |
2675 |
Familial thrombotic thrombocytopenic purpura (TTP) |
2681 |
Nephropathy due to eclampsia |
2699 |
Sickle cell nephropathy - no histology |
2702 |
Sickle cell nephropathy - histologically proven |
3380 |
Acute kidney injury |
3398 |
Acute kidney injury due to hypovolaemia |
3403 |
Acute kidney injury due to circulatory failure |
3419 |
Acute kidney injury due to sepsis |
3426 |
Acute kidney injury due to rhabdomyolysis |
3435 |
Acute kidney injury due to nephrotoxicity |
3442 |
Acute cortical necrosis |
3461 |
Kidney tumour |
3474 |
Renal cell carcinoma - histologically proven |
3488 |
Transitional cell carcinoma - histologically proven |
3490 |
Wilms tumour - histologically proven |
3501 |
Mesoblastic nephroma - histologically proven |
3529 |
Chronic kidney disease (CKD) / chronic renal failure (CRF) caused by tumour nephrectomy |
3538 |
Chronic kidney disease (CKD) / chronic renal failure (CRF) due to traumatic loss of kidney |
3643 |
Chronic renal failure due to systemic infection |
2316 |
Diabetic nephropathy in type I diabetes - no histology |
2328 |
Diabetic nephropathy in type I diabetes - histologically proven |
2337 |
Diabetic nephropathy in type II diabetes - no histology |
2344 |
Diabetic nephropathy in type II diabetes - histologically proven |
3139 |
Inherited / genetic diabetes mellitus type II |
3627 |
Renal cysts and diabetes syndrome |
2476 |
Renal vein thrombosis |
2773 |
Benign familial haematuria |
2787 |
Thin basement membrane disease |
3517 |
Single kidney identified in adulthood |
3540 |
Chronic kidney disease (CKD) / chronic renal failure (CRF) due
to donor nephrectomy |
3555 |
Chronic kidney disease (CKD) / chronic renal failure (CRF) -
aetiology uncertain / unknown - no histology |
3564 |
Chronic kidney disease (CKD) / chronic renal failure (CRF) -
aetiology uncertain / unknown - histologically proven |
3572 |
Haematuria and proteinuria - no histology |
3712 |
Isolated haematuria - no histology |
3720 |
Isolated proteinuria - no histology |
3691 |
Renal failure |
3708 |
Chronic renal failure |